L-Phenylalanine CAS:63-91-2 99% Te paura ma
| Nama Putumōhio | XD90317 |
| Ingoa Hua | L-Cysteine hydrochloride anhydrous |
| CAS | 63-91-2 |
| Tātai rāpoi | C9H11NO2 |
| Taumaha rāpoi | 165.19 |
| Nga Taipitopito Rokiroki | Ambient |
| Waehere Rere Whakariterite | 29224985 |
Whakatakotoranga Hua
| Te ahua | Te paura tioata ma |
| Te whakamatautau | 99% |
| Te hurihanga motuhake | -20.4 ki -35.2 |
| Nga konganuku taumaha | <0.002% |
| Arataki | <10mg/kg |
| pH | 5.4 - 6 |
| Ngaronga i te whakamaroke | <0.40% |
| Te toenga i runga i te mura | <0.10% |
I roto i te maple tirikara mimi mate (MSUD), manga-mekameka L-amino (BCAA) me te 2-oxo acids (BCOA) ka whakaemi i roto i nga wai o te tinana na te ngoikoretanga o te mekameka manga 2-oxo acid dehydrogenase mahi matatini.I roto i te MSUD, he iti noa nga korero e waatea ana mo te hiranga o te tuku mimi o nga puhui mekameka-manga.I tirotirohia e matou te whakakorenga renal o te leucine, valine, isoleucine me te alloisoleucine, me o ratou waikawa 2-oxo 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S)-(S- KMV), me (R) -3-methyl-2-oxopentanoate (R-KMV), ma te whakamahi takirua o te plasma me te mimi tauira (n = 63) mai i nga turoro 10 me te MSUD tawhito.Ko te hautanga renal excretion o BCAA kore utu i roto i te awhe noa (< 0.5%) me te motuhake o nga kukume plasma.Ko te whakakorenga o te BCAA herea (N-acylated) he mea noa me te kore e tino whakawhirinaki ki nga kohinga plasma BCAA.Ko te hautanga renal excretion o BCOA i roto i te raupapa KIC << KIV < R-KMV < or = S-KMV (awhe (%): KIC 0.1-25; KI V 0.14-21.3; S-KMV 0.26-24.6; R- Ko te KMV 0.1-35.9), he tino hono ki nga kohinga plasma KIC, me te nuinga teitei ake i tera o te BCAA e pa ana.Ko nga hua e whakaatu ana ko te tangohanga o nga whatukuhu o te BCAA kore utu tae atu ki nga hua o te acylated he iti noa.Heoi, ko te whakakorenga o te renal o te BCOA, he aukati i te piki haere o nga kuhanga BCAA, na reira ka whai waahi ki te whakaheke i nga puna BCAA katoa i roto i te MSUD.
